ACR Appropriateness Criteria® Congenital or Acquired Heart Disease

Expert Panels on Cardiac Imaging and Pediatric Imaging

Research output: Contribution to journalArticlepeer-review


Pediatric heart disease is a large and diverse field with an overall prevalence estimated at 6 to 13 per 1,000 live births. This document discusses appropriateness of advanced imaging for a broad range of variants. Diseases covered include tetralogy of Fallot, transposition of great arteries, congenital or acquired pediatric coronary artery abnormality, single ventricle, aortopathy, anomalous pulmonary venous return, aortopathy and aortic coarctation, with indications for advanced imaging spanning the entire natural history of the disease in children and adults, including initial diagnosis, treatment planning, treatment monitoring, and early detection of complications. The American College of Radiology Appropriateness Criteria are evidence-based guidelines for specific clinical conditions that are reviewed annually by a multidisciplinary expert panel. The guideline development and revision process support the systematic analysis of the medical literature from peer reviewed journals. Established methodology principles such as Grading of Recommendations Assessment, Development, and Evaluation or GRADE are adapted to evaluate the evidence. The RAND/UCLA Appropriateness Method User Manual provides the methodology to determine the appropriateness of imaging and treatment procedures for specific clinical scenarios. In those instances where peer reviewed literature is lacking or equivocal, experts may be the primary evidentiary source available to formulate a recommendation.

Original languageEnglish (US)
Pages (from-to)S351-S381
JournalJournal of the American College of Radiology
Issue number11
StatePublished - Nov 2023


  • AUC
  • Appropriateness Criteria
  • anomalous pulmonary venous return
  • aortopathy
  • appropriate use criteria
  • arterial switch operation
  • atrial switch operation
  • coarctation
  • congenital heart disease
  • connective tissue disease
  • coronary artery
  • imaging
  • pediatric heart disease
  • single ventricle
  • tetralogy of Fallot
  • transposition of great arteries

ASJC Scopus subject areas

  • Radiology Nuclear Medicine and imaging


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