Background context: Diastematomyelia is a split-cord malformation often accompanied by other cord or column anomalies. Purpose: To report on an adult patient with diastematomyelia and discuss the embryological basis and related developmental sequelae of this split-cord malformation. Study design: Case report. Methods: A summary of the management of a 54-year-old woman with recent clinical symptomatology related to an undiagnosed split-cord malformation is presented with accompanying literature review. Results: A rare adult presentation of diastematomyelia with accompanying intradural extramedullary epidermoid tumor was repaired with resection of the soft-tissue mass and excision of the fibro-osseous septum. Conclusion: Initial presentation of diastematomyelia is rarely seen in adults; accompanying pathology includes scoliosis, tethered cord, and intradural tumors. Effective treatment involves identification of the primary pathology.
- Adult presentation
- Intradural extramedullary epidermoid tumor
- Tethered cord
- Type I split-cord malformation
ASJC Scopus subject areas
- Orthopedics and Sports Medicine
- Clinical Neurology