Cardiac sarcoidosis masquerading as right ventricular dysplasia

Peter Ott*, Frank I. Marcus, Richard E. Sobonya, Fred Morady, Bradley P. Knight, Charles E. Fuenzalida

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

67 Scopus citations

Abstract

Patients with cardiac sarcoidosis may present with clinical and morphological features similar to arrhythmogenic right ventricular dysplasia (ARVD) or cardiomyopathy (ARVC). Three cases of cardiac sarcoidosis are presented that clinically mimicked ARVD or ARVC until a pathology diagnosis of sarcoidosis was made at biopsy or autopsy. A diagnostic distinction, while often difficult to make, is important since treatment with corticosteroids may benefit those with sarcoidosis but is not expected to be useful in cases with ARVD or ARVC.

Original languageEnglish (US)
Pages (from-to)1498-1503
Number of pages6
JournalPACE - Pacing and Clinical Electrophysiology
Volume26
Issue number7 I
DOIs
StatePublished - Jul 1 2003

Keywords

  • Arrhythmogenic right ventricular dysplasia/cardiomyopathy
  • Sarcoidosis
  • Ventricular tachycardia

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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