Dermatofibrosarcoma protuberans and the bednar tumor: Treatment in the pediatric population

Jeffrey R. Marcus*, Julius W. Few, Christof Senger, Marleta Reynolds

*Corresponding author for this work

Research output: Contribution to journalArticle

29 Scopus citations

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a low-intermediate-grade cutaneous sarcoma that has a marked propensity for local recurrence after excision. The Bednar variant of this tumor is even less common and is distinguished histologically by the dispersal of melanin containing cells in an otherwise typical DFSP. Both are considered to be tumors of the third and forth decades of life, but both DFSP and the Bednar variant have been described in children. Until this report of a congenital Bednar tumor, only the DFSP has also been described in the neonate. The histopathology and surgical management of DFSP and Bednar tumors are outlined with emphasis on reported experience in the pediatric population. The surgical management of these lesions in children is based on numerous series in adults and the limited pediatric experience. The recommended treatment is wide excision with 3-cm margins of visibly uninvolved tissue and inclusion of superficial fascia.

Original languageEnglish (US)
Pages (from-to)1811-1814
Number of pages4
JournalJournal of pediatric surgery
Volume33
Issue number12
DOIs
StatePublished - Dec 1998

Keywords

  • Bednar tumor
  • Dermatofibrosarcoma protuberans
  • Treatment

ASJC Scopus subject areas

  • Surgery
  • Pediatrics, Perinatology, and Child Health

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