Development of nonspecific interstitial pneumonitis associated with long-term treatment of primary pulmonary hypertension with prostacyclin

Steven Kesten*, John Dainauskas, Vallerie McLaughlin, Stuart Rich

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

19 Scopus citations

Abstract

A young woman with primary pulmonary hypertension presented with interstitial lung disease approximately 5 years after successful treatment with IV prostacyclin. The pathology was consistent with nonspecific interstitial pneumonitis and was unresponsive to steroids and immunosuppressive medications. We speculate that further cases of this syndrome may be reported as more patients are living beyond 5 years with prostacyclin.

Original languageEnglish (US)
Pages (from-to)566-569
Number of pages4
JournalCHEST
Volume116
Issue number2
DOIs
StatePublished - 1999

Keywords

  • Interstitial lung disease
  • Primary pulmonary hypertension
  • Prostacyclin

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine
  • Critical Care and Intensive Care Medicine
  • Cardiology and Cardiovascular Medicine

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