Diagnostic and surgical challenge: Middle ear dermoid cyst in 12 month old with branchio-oto-renal syndrome and multiple middle-ear congenital anomalies

D. R. Johnston*, K. Whittemore, D. Poe, C. D. Robson, A. R. Perez-Atayde

*Corresponding author for this work

Research output: Contribution to journalArticle

2 Scopus citations

Abstract

Described is the first case report, to our knowledge, of a middle-ear dermoid in a child with branchio-oto-renal (BOR) syndrome. Radiographic, pathologic, and intraoperative figures are shown. This was a diagnostic and surgical challenge as the presentation was similar to a congenital cholesteatoma and the child had numerous significant temporal bone abnormalities. After the intraoperative findings suggested a non-destructive process, the treatment strategy was altered. This case reiterates the need for a cautious, flexible operative approach in a syndromic child. Included is a relevant review of the literature and a detailed clinical analysis.

Original languageEnglish (US)
Pages (from-to)1341-1345
Number of pages5
JournalInternational Journal of Pediatric Otorhinolaryngology
Volume75
Issue number10
DOIs
StatePublished - Oct 1 2011

Keywords

  • Branchio-oto-renal syndrome
  • Congenital cholesteatoma
  • Dermoid cyst
  • Hairy cyst
  • Hairy polyp
  • Teratoma

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Otorhinolaryngology

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