Endocardial cushion defect associated with cor triatriatum sinistrum or supravalve mitral ring

Otto G. Thilenius*, Dolores Vitullo, Saroja Bharati, Julia Luken, John J. Lamberti, Constantine Tatooles, Maurice Lev, Ian Carr, Rene A. Arcilla

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

12 Scopus citations


Clinical and angiographic or autopsy data, or both, on three children with a subdivided left atrium (cor triatriatum) and an associated endocardial cushion defect are reviewed. (One child had ostium primum defect, and two had complete atrioventricular [A-V] canal.) A fourth patient demonstrates the difficulties in differentiating subdivided left atrium from supravalve mitral stenosis in the presence of an endocardial cushion defect. The clinical findings are greatly influenced by the endocardial cushion defect. A pressure gradient between the pulmonary wedge and (left or right) ventricular end-diastolic pressures in patients with an endocardial cushion defect indicates pulmonary venous obstruction and should alert one to the possibility of these combined lesions. The exact diagnosis is made with injections of angiographic contrast medium into the proximal and distal left atrial chambers, to document the respective relations of the pulmonary veins, left atrial appendage and A-V valves to these atrial chambers. All three patients with an endocardial cushion defect and a subdivided left atrium had an associated patent ductus arteriosus. The common association of subdivided left atrium with intracardiac, pulmonary venous and aortic anomalies is again demonstrated.

Original languageEnglish (US)
Pages (from-to)1339-1343
Number of pages5
JournalThe American journal of cardiology
Issue number7
StatePublished - Dec 1979

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine


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