Epidural spinal involvement of Erdheim-Chester disease causing myelopathy

Brian Y. Hwang; Ann Liu; Jason Kern; C. Rory Goodwin; Jean Paul Wolinsky; Atman Desai

doi:10.1016/j.jocn.2015.04.004

Epidural spinal involvement of Erdheim-Chester disease causing myelopathy

Brian Y. Hwang, Ann Liu, Jason Kern, C. Rory Goodwin, Jean Paul Wolinsky, Atman Desai^*

^*Corresponding author for this work

Neurological Surgery

Research output: Contribution to journal › Article › peer-review

7 Scopus citations

Abstract

We present a 25-year-old woman with Erdheim-Chester disease (ECD) presenting with progressive myelopathy from multiple compressive spinal epidural lesions who required cervicothoracic decompression and fusion, and summarize the literature on epidural spinal involvement of ECD. ECD is a rare non-Langerhans histiocytosis affecting multiple organ systems through infiltration and characteristically causing multifocal osteosclerosis. Central nervous system involvement, particularly of the spine, is rare.

Original language	English (US)
Pages (from-to)	1532-1536
Number of pages	5
Journal	Journal of Clinical Neuroscience
Volume	22
Issue number	9
DOIs	https://doi.org/10.1016/j.jocn.2015.04.004
State	Published - 2015

Keywords

Epidural
Erdheim-Chester disease
Non-Langerhans histiocytosis
Spine

ASJC Scopus subject areas

Clinical Neurology
Neurology
Physiology (medical)
Surgery

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10.1016/j.jocn.2015.04.004

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title = "Epidural spinal involvement of Erdheim-Chester disease causing myelopathy",

abstract = "We present a 25-year-old woman with Erdheim-Chester disease (ECD) presenting with progressive myelopathy from multiple compressive spinal epidural lesions who required cervicothoracic decompression and fusion, and summarize the literature on epidural spinal involvement of ECD. ECD is a rare non-Langerhans histiocytosis affecting multiple organ systems through infiltration and characteristically causing multifocal osteosclerosis. Central nervous system involvement, particularly of the spine, is rare.",

keywords = "Epidural, Erdheim-Chester disease, Non-Langerhans histiocytosis, Spine",

author = "Hwang, \{Brian Y.\} and Ann Liu and Jason Kern and Goodwin, \{C. Rory\} and Wolinsky, \{Jean Paul\} and Atman Desai",

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language = "English (US)",

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T1 - Epidural spinal involvement of Erdheim-Chester disease causing myelopathy

AU - Hwang, Brian Y.

AU - Liu, Ann

AU - Kern, Jason

AU - Goodwin, C. Rory

AU - Wolinsky, Jean Paul

AU - Desai, Atman

PY - 2015

Y1 - 2015

N2 - We present a 25-year-old woman with Erdheim-Chester disease (ECD) presenting with progressive myelopathy from multiple compressive spinal epidural lesions who required cervicothoracic decompression and fusion, and summarize the literature on epidural spinal involvement of ECD. ECD is a rare non-Langerhans histiocytosis affecting multiple organ systems through infiltration and characteristically causing multifocal osteosclerosis. Central nervous system involvement, particularly of the spine, is rare.

AB - We present a 25-year-old woman with Erdheim-Chester disease (ECD) presenting with progressive myelopathy from multiple compressive spinal epidural lesions who required cervicothoracic decompression and fusion, and summarize the literature on epidural spinal involvement of ECD. ECD is a rare non-Langerhans histiocytosis affecting multiple organ systems through infiltration and characteristically causing multifocal osteosclerosis. Central nervous system involvement, particularly of the spine, is rare.

KW - Epidural

KW - Erdheim-Chester disease

KW - Non-Langerhans histiocytosis

KW - Spine

UR - https://www.scopus.com/pages/publications/84945450727

UR - https://www.scopus.com/inward/citedby.url?scp=84945450727&partnerID=8YFLogxK

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AN - SCOPUS:84945450727

SN - 0967-5868

VL - 22

SP - 1532

EP - 1536

JO - Journal of Clinical Neuroscience

JF - Journal of Clinical Neuroscience

IS - 9

ER -

Epidural spinal involvement of Erdheim-Chester disease causing myelopathy

Abstract

Keywords

ASJC Scopus subject areas

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