Fibroinflammatory tumor of the liver causing biliary cirrhosis in an infant

Estella M. Alonso; Teresita M. Zdunek; Marilyn R. Brown; David K. Yousefzadeh; Peter F. Whitington

doi:10.1097/00005176-199102000-00025

Fibroinflammatory tumor of the liver causing biliary cirrhosis in an infant

Estella M. Alonso, Teresita M. Zdunek, Marilyn R. Brown, David K. Yousefzadeh, Peter F. Whitington^*

^*Corresponding author for this work

Pediatrics

Research output: Contribution to journal › Article › peer-review

3 Scopus citations

Abstract

We report the case of a 21-month-old child with a fibroinflammatory tumor of the liver causing biliary obstruction. The patient had fever, diarrhea, and jaundice. Abdominal ultrasonography, computerized tomography, and endoscopic retrograde cholangiopancreatography demonstrated the tumor to be in the porta hepatis. Growth of the mass resulted in destruction of the common hepatic duct, and chronic obstruction led to biliary cirrhosis over 4 months’ time. Histologic study of the tumor revealed a fibrous stroma infiltrated by inflammatory cells. The patient was successfully treated with an orthotopic liver transplantation and is doing well 18 months following initial diagnosis without evidence of recurrence.

Original language	English (US)
Pages (from-to)	283-287
Number of pages	5
Journal	Journal of pediatric gastroenterology and nutrition
Volume	12
Issue number	2
DOIs	https://doi.org/10.1097/00005176-199102000-00025
State	Published - Feb 1991

Keywords

Biliary cirrhosis
Fibroinflammatory tumor

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Gastroenterology

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

Access to Document

10.1097/00005176-199102000-00025

Cite this

@article{64b234251448495bbda14cd23db6af97,

title = "Fibroinflammatory tumor of the liver causing biliary cirrhosis in an infant",

abstract = "We report the case of a 21-month-old child with a fibroinflammatory tumor of the liver causing biliary obstruction. The patient had fever, diarrhea, and jaundice. Abdominal ultrasonography, computerized tomography, and endoscopic retrograde cholangiopancreatography demonstrated the tumor to be in the porta hepatis. Growth of the mass resulted in destruction of the common hepatic duct, and chronic obstruction led to biliary cirrhosis over 4 months{\textquoteright} time. Histologic study of the tumor revealed a fibrous stroma infiltrated by inflammatory cells. The patient was successfully treated with an orthotopic liver transplantation and is doing well 18 months following initial diagnosis without evidence of recurrence.",

keywords = "Biliary cirrhosis, Fibroinflammatory tumor",

author = "Alonso, {Estella M.} and Zdunek, {Teresita M.} and Brown, {Marilyn R.} and Yousefzadeh, {David K.} and Whitington, {Peter F.}",

year = "1991",

month = feb,

doi = "10.1097/00005176-199102000-00025",

language = "English (US)",

volume = "12",

pages = "283--287",

journal = "Journal of pediatric gastroenterology and nutrition",

issn = "0277-2116",

publisher = "Lippincott Williams and Wilkins",

number = "2",

}

TY - JOUR

T1 - Fibroinflammatory tumor of the liver causing biliary cirrhosis in an infant

AU - Alonso, Estella M.

AU - Zdunek, Teresita M.

AU - Brown, Marilyn R.

AU - Yousefzadeh, David K.

AU - Whitington, Peter F.

PY - 1991/2

Y1 - 1991/2

N2 - We report the case of a 21-month-old child with a fibroinflammatory tumor of the liver causing biliary obstruction. The patient had fever, diarrhea, and jaundice. Abdominal ultrasonography, computerized tomography, and endoscopic retrograde cholangiopancreatography demonstrated the tumor to be in the porta hepatis. Growth of the mass resulted in destruction of the common hepatic duct, and chronic obstruction led to biliary cirrhosis over 4 months’ time. Histologic study of the tumor revealed a fibrous stroma infiltrated by inflammatory cells. The patient was successfully treated with an orthotopic liver transplantation and is doing well 18 months following initial diagnosis without evidence of recurrence.

AB - We report the case of a 21-month-old child with a fibroinflammatory tumor of the liver causing biliary obstruction. The patient had fever, diarrhea, and jaundice. Abdominal ultrasonography, computerized tomography, and endoscopic retrograde cholangiopancreatography demonstrated the tumor to be in the porta hepatis. Growth of the mass resulted in destruction of the common hepatic duct, and chronic obstruction led to biliary cirrhosis over 4 months’ time. Histologic study of the tumor revealed a fibrous stroma infiltrated by inflammatory cells. The patient was successfully treated with an orthotopic liver transplantation and is doing well 18 months following initial diagnosis without evidence of recurrence.

KW - Biliary cirrhosis

KW - Fibroinflammatory tumor

UR - http://www.scopus.com/inward/record.url?scp=0025854834&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=0025854834&partnerID=8YFLogxK

U2 - 10.1097/00005176-199102000-00025

DO - 10.1097/00005176-199102000-00025

M3 - Article

C2 - 2051282

AN - SCOPUS:0025854834

SN - 0277-2116

VL - 12

SP - 283

EP - 287

JO - Journal of pediatric gastroenterology and nutrition

JF - Journal of pediatric gastroenterology and nutrition

IS - 2

ER -

Fibroinflammatory tumor of the liver causing biliary cirrhosis in an infant

Abstract

Keywords

ASJC Scopus subject areas

UN SDGs

Access to Document

Other files and links

Fingerprint

Cite this