Fibrous Dysplasia and Juvenile Psammomatoid Ossifying Fibroma: A Case of Mistaken Identity

Sergey Y. Turin, Chad Purnell, Arun K. Gosain*

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

Abstract

Juvenile psammomatoid ossifying fibroma (JPOF) is a rare benign osseous tumor, usually presenting in the midface. There are many similarities in location, presentation, and radiographic appearance between fibrous dysplasia (FD) and JPOF. Awareness of this entity is important for craniofacial surgeons, as surgical timing and intraoperative management differ between these tumors. Findings that should raise suspicion of JPOF preoperatively include rapid growth, a shell of cortical bone surrounding the lesion, and clearly demarcated borders of the lesion on imaging, as opposed to a gradual transition between normal and abnormal bone. Definitive excision is the treatment of choice, and earlier surgery may provide better results by addressing the lesion at the smallest size possible. In contrast to FD, JPOF is not known to “burn out,” so there is minimal benefit to be gained from delay. We present a summary of the evidence for diagnosis and treatment of JPOF as well our experience with JPOF in an 11-year-old female who was initially diagnosed with FD. We aim to draw attention to the similar presentations of these entities so the reader will be able to more accurately manage these patients.

Original languageEnglish (US)
Pages (from-to)1083-1088
Number of pages6
JournalCleft Palate-Craniofacial Journal
Volume56
Issue number8
DOIs
StatePublished - Sep 1 2019
Externally publishedYes

Keywords

  • craniofacial growth
  • craniofacial morphology
  • facial morphology
  • magnetic resonance imaging
  • maxilla
  • midfacial growth
  • scarring
  • skeletal morphology
  • surgical complications
  • surgical technique

ASJC Scopus subject areas

  • Oral Surgery
  • Otorhinolaryngology

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