Abstract
Two children developed hepatoblastoma concurrent with congenital portosystemic shunts (PSSs) (Abernethy malformations). Both underwent operative ligation of their PSSs. One received concurrent tumor resection, whereas the other was deemed initially unresectable and underwent biopsy followed by neoadjuvant chemotherapy. Although benign hepatic masses, such as focal nodular hyperplasia and nodular regenerative hyperplasia, are common in patients with Abernethy malformations, malignant tumors have also been documented and should always be considered in the differential diagnosis of a patient with a congenital PSS and a hepatic mass.
| Original language | English (US) |
|---|---|
| Pages (from-to) | 542-545 |
| Number of pages | 4 |
| Journal | Journal of pediatric gastroenterology and nutrition |
| Volume | 62 |
| Issue number | 4 |
| DOIs | |
| State | Published - Jan 1 2016 |
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Keywords
- Abernethy malformation
- Hepatoblastoma
- Portosystemic shunt
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health
- Gastroenterology
Cite this
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Hepatoblastoma in children with congenital portosystemic shunts. / Lautz, Timothy B; Shah, Sonam A.; Superina, Riccardo A.
In: Journal of pediatric gastroenterology and nutrition, Vol. 62, No. 4, 01.01.2016, p. 542-545.Research output: Contribution to journal › Article
TY - JOUR
T1 - Hepatoblastoma in children with congenital portosystemic shunts
AU - Lautz, Timothy B
AU - Shah, Sonam A.
AU - Superina, Riccardo A
PY - 2016/1/1
Y1 - 2016/1/1
N2 - Two children developed hepatoblastoma concurrent with congenital portosystemic shunts (PSSs) (Abernethy malformations). Both underwent operative ligation of their PSSs. One received concurrent tumor resection, whereas the other was deemed initially unresectable and underwent biopsy followed by neoadjuvant chemotherapy. Although benign hepatic masses, such as focal nodular hyperplasia and nodular regenerative hyperplasia, are common in patients with Abernethy malformations, malignant tumors have also been documented and should always be considered in the differential diagnosis of a patient with a congenital PSS and a hepatic mass.
AB - Two children developed hepatoblastoma concurrent with congenital portosystemic shunts (PSSs) (Abernethy malformations). Both underwent operative ligation of their PSSs. One received concurrent tumor resection, whereas the other was deemed initially unresectable and underwent biopsy followed by neoadjuvant chemotherapy. Although benign hepatic masses, such as focal nodular hyperplasia and nodular regenerative hyperplasia, are common in patients with Abernethy malformations, malignant tumors have also been documented and should always be considered in the differential diagnosis of a patient with a congenital PSS and a hepatic mass.
KW - Abernethy malformation
KW - Hepatoblastoma
KW - Portosystemic shunt
UR - http://www.scopus.com/inward/record.url?scp=84944755374&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=84944755374&partnerID=8YFLogxK
U2 - 10.1097/MPG.0000000000001012
DO - 10.1097/MPG.0000000000001012
M3 - Article
VL - 62
SP - 542
EP - 545
JO - Journal of Pediatric Gastroenterology and Nutrition
JF - Journal of Pediatric Gastroenterology and Nutrition
SN - 0277-2116
IS - 4
ER -