Hypersensitive carotid sinus syndrome due to neurofibromatosis-1 and manifested by repeated episodes of syncope

Jessica A. Sutherland, Paul Stobie, Vijay Swarup, Sean P. Tierney, Albert C. Lin, Martin C. Burke*

*Corresponding author for this work

Research output: Contribution to journalArticle

4 Scopus citations

Abstract

A 28-year-old patient with neurofibromatosis-1 presented with syncope. The exam demonstrated a mass adjacent and inferior to the right occiput that extended to the posterior lateral right-sided neck. Initial invasive and noninvasive testing was negative. Imaging of her head and neck demonstrated a large neurofibroma enveloping her right carotid sinus without vessel occlusion or evidence of malignancy. An event recorder documented asystole. A pacemaker was implanted to avoid the surgical morbidity of removing the neck mass. The patient has since been free of syncope. We believe neurofibromatosis-1 should be included in the differential of syncope.

Original languageEnglish (US)
Pages (from-to)1571-1573
Number of pages3
JournalPACE - Pacing and Clinical Electrophysiology
Volume27
Issue number11
DOIs
StatePublished - Nov 1 2004

Keywords

  • Hypersensitive carotid sinus
  • Neurofibromatosis-1
  • Syncope

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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