Hypoplastic left heart syndrome associated with large omphalocele and hypoplastic left bronchus

Michael Hainstock; Dianna Bardo; Mary Rice; Stephen Langley

doi:10.1007/s00246-010-9716-7

Hypoplastic left heart syndrome associated with large omphalocele and hypoplastic left bronchus

Michael Hainstock^*, Dianna Bardo, Mary Rice, Stephen Langley

^*Corresponding author for this work

Radiology

Research output: Contribution to journal › Article › peer-review

5 Scopus citations

Abstract

We present a patient with the combination of hypoplastic left heart syndrome (HLHS), large omphalocele, and hypoplastic left bronchus who underwent a modified Norwood procedure and was successfully discharged home. The child required tracheostomy with home ventilation and we elected to delay the primary repair of the omphalocele. To our knowledge, this is the first reported case with this combination of anomalies surviving till hospital discharge. Our experience demonstrates the potential viability of patients with concurrent HLHS, large abdominal wall defects, and airway anomalies and may additionally advocate for delayed repair of large omphaloceles in patients with complex congenital heart disease.

Original language	English (US)
Pages (from-to)	878-880
Number of pages	3
Journal	Pediatric cardiology
Volume	31
Issue number	6
DOIs	https://doi.org/10.1007/s00246-010-9716-7
State	Published - Aug 2010

Keywords

Hypoplastic bronchus
Hypoplastic left heart syndrome
Omphalocele
Single ventricle

ASJC Scopus subject areas

Cardiology and Cardiovascular Medicine
Pediatrics, Perinatology, and Child Health

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

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10.1007/s00246-010-9716-7

Cite this

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title = "Hypoplastic left heart syndrome associated with large omphalocele and hypoplastic left bronchus",

abstract = "We present a patient with the combination of hypoplastic left heart syndrome (HLHS), large omphalocele, and hypoplastic left bronchus who underwent a modified Norwood procedure and was successfully discharged home. The child required tracheostomy with home ventilation and we elected to delay the primary repair of the omphalocele. To our knowledge, this is the first reported case with this combination of anomalies surviving till hospital discharge. Our experience demonstrates the potential viability of patients with concurrent HLHS, large abdominal wall defects, and airway anomalies and may additionally advocate for delayed repair of large omphaloceles in patients with complex congenital heart disease.",

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T1 - Hypoplastic left heart syndrome associated with large omphalocele and hypoplastic left bronchus

AU - Hainstock, Michael

AU - Bardo, Dianna

AU - Rice, Mary

AU - Langley, Stephen

PY - 2010/8

Y1 - 2010/8

N2 - We present a patient with the combination of hypoplastic left heart syndrome (HLHS), large omphalocele, and hypoplastic left bronchus who underwent a modified Norwood procedure and was successfully discharged home. The child required tracheostomy with home ventilation and we elected to delay the primary repair of the omphalocele. To our knowledge, this is the first reported case with this combination of anomalies surviving till hospital discharge. Our experience demonstrates the potential viability of patients with concurrent HLHS, large abdominal wall defects, and airway anomalies and may additionally advocate for delayed repair of large omphaloceles in patients with complex congenital heart disease.

AB - We present a patient with the combination of hypoplastic left heart syndrome (HLHS), large omphalocele, and hypoplastic left bronchus who underwent a modified Norwood procedure and was successfully discharged home. The child required tracheostomy with home ventilation and we elected to delay the primary repair of the omphalocele. To our knowledge, this is the first reported case with this combination of anomalies surviving till hospital discharge. Our experience demonstrates the potential viability of patients with concurrent HLHS, large abdominal wall defects, and airway anomalies and may additionally advocate for delayed repair of large omphaloceles in patients with complex congenital heart disease.

KW - Hypoplastic bronchus

KW - Hypoplastic left heart syndrome

KW - Omphalocele

KW - Single ventricle

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ER -

Hypoplastic left heart syndrome associated with large omphalocele and hypoplastic left bronchus

Abstract

Keywords

ASJC Scopus subject areas

UN SDGs

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