International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes

Hector I. Michelena; Alessandro Della Corte; Arturo Evangelista; Joseph J. Maleszewski; William D. Edwards; Mary J. Roman; Richard B. Devereux; Borja Fernández; Federico M. Asch; Alex J. Barker; Lilia M. Sierra-Galan; Laurent De Kerchove; Susan M. Fernandes; Paul W.M. Fedak; Evaldas Girdauskas; Victoria Delgado; Suhny Abbara; Emmanuel Lansac; Siddharth K. Prakash; Malenka M. Bissell; Bogdan A. Popescu; Michael D. Hope; Marta Sitges; Vinod H. Thourani; Phillippe Pibarot; Krishnaswamy Chandrasekaran; Patrizio Lancellotti; Michael A. Borger; John K. Forrest; John Webb; Dianna M. Milewicz; Raj Makkar; Martin B. Leon; Stephen P. Sanders; Michael Markl; Victor A. Ferrari; William C. Roberts; Jae Kwan Song; Philipp Blanke; Charles S. White; Samuel Siu; Lars G. Svensson; Alan C. Braverman; Joseph Bavaria; Thoralf M. Sundt; Gebrine El Khoury; Ruggero De Paulis; Maurice Enriquez-Sarano; Jeroen J. Bax; Catherine M. Otto; Hans Joachim Schäfers

doi:10.1093/ejcts/ezab038

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes

Hector I. Michelena^*, Alessandro Della Corte, Arturo Evangelista, Joseph J. Maleszewski, William D. Edwards, Mary J. Roman, Richard B. Devereux, Borja Fernández, Federico M. Asch, Alex J. Barker, Lilia M. Sierra-Galan, Laurent De Kerchove, Susan M. Fernandes, Paul W.M. Fedak, Evaldas Girdauskas, Victoria Delgado, Suhny Abbara, Emmanuel Lansac, Siddharth K. Prakash, Malenka M. BissellBogdan A. Popescu, Michael D. Hope, Marta Sitges, Vinod H. Thourani, Phillippe Pibarot, Krishnaswamy Chandrasekaran, Patrizio Lancellotti, Michael A. Borger, John K. Forrest, John Webb, Dianna M. Milewicz, Raj Makkar, Martin B. Leon, Stephen P. Sanders, Michael Markl, Victor A. Ferrari, William C. Roberts, Jae Kwan Song, Philipp Blanke, Charles S. White, Samuel Siu, Lars G. Svensson, Alan C. Braverman, Joseph Bavaria, Thoralf M. Sundt, Gebrine El Khoury, Ruggero De Paulis, Maurice Enriquez-Sarano, Jeroen J. Bax, Catherine M. Otto, Hans Joachim Schäfers

^*Corresponding author for this work

Radiology

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Abstract

This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.

Original language	English (US)
Pages (from-to)	448-476
Number of pages	29
Journal	European Journal of Cardio-thoracic Surgery
Volume	60
Issue number	3
DOIs	https://doi.org/10.1093/ejcts/ezab038
State	Published - Sep 1 2021

Keywords

Aortopathy
Bicuspid aortic valve
Classification
Nomenclature

ASJC Scopus subject areas

Surgery
Pulmonary and Respiratory Medicine
Cardiology and Cardiovascular Medicine

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

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10.1093/ejcts/ezab038

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Michelena, H. I., Della Corte, A., Evangelista, A., Maleszewski, J. J., Edwards, W. D., Roman, M. J., Devereux, R. B., Fernández, B., Asch, F. M., Barker, A. J., Sierra-Galan, L. M., De Kerchove, L., Fernandes, S. M., Fedak, P. W. M., Girdauskas, E., Delgado, V., Abbara, S., Lansac, E., Prakash, S. K., ... Schäfers, H. J. (2021). International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes. European Journal of Cardio-thoracic Surgery, 60(3), 448-476. https://doi.org/10.1093/ejcts/ezab038

@article{84070bb3696f482c9bb5e8825bbac515,

title = "International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes",

abstract = "This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.",

keywords = "Aortopathy, Bicuspid aortic valve, Classification, Nomenclature",

author = "Michelena, \{Hector I.\} and \{Della Corte\}, Alessandro and Arturo Evangelista and Maleszewski, \{Joseph J.\} and Edwards, \{William D.\} and Roman, \{Mary J.\} and Devereux, \{Richard B.\} and Borja Fern{\'a}ndez and Asch, \{Federico M.\} and Barker, \{Alex J.\} and Sierra-Galan, \{Lilia M.\} and \{De Kerchove\}, Laurent and Fernandes, \{Susan M.\} and Fedak, \{Paul W.M.\} and Evaldas Girdauskas and Victoria Delgado and Suhny Abbara and Emmanuel Lansac and Prakash, \{Siddharth K.\} and Bissell, \{Malenka M.\} and Popescu, \{Bogdan A.\} and Hope, \{Michael D.\} and Marta Sitges and Thourani, \{Vinod H.\} and Phillippe Pibarot and Krishnaswamy Chandrasekaran and Patrizio Lancellotti and Borger, \{Michael A.\} and Forrest, \{John K.\} and John Webb and Milewicz, \{Dianna M.\} and Raj Makkar and Leon, \{Martin B.\} and Sanders, \{Stephen P.\} and Michael Markl and Ferrari, \{Victor A.\} and Roberts, \{William C.\} and Song, \{Jae Kwan\} and Philipp Blanke and White, \{Charles S.\} and Samuel Siu and Svensson, \{Lars G.\} and Braverman, \{Alan C.\} and Joseph Bavaria and Sundt, \{Thoralf M.\} and \{El Khoury\}, Gebrine and \{De Paulis\}, Ruggero and Maurice Enriquez-Sarano and Bax, \{Jeroen J.\} and Otto, \{Catherine M.\} and Sch{\"a}fers, \{Hans Joachim\}",

note = "Publisher Copyright: {\textcopyright} 2021 Jointly between the European Association for Cardio-Thoracic Surgery, The Society of Thoracic Surgeons, the American Association for Thoracic Surgery, and the Radiological Society of North America.",

year = "2021",

month = sep,

day = "1",

doi = "10.1093/ejcts/ezab038",

language = "English (US)",

volume = "60",

pages = "448--476",

journal = "European Journal of Cardio-thoracic Surgery",

issn = "1010-7940",

publisher = "European Association for Cardio-Thoracic Surgery",

number = "3",

}

Michelena, HI, Della Corte, A, Evangelista, A, Maleszewski, JJ, Edwards, WD, Roman, MJ, Devereux, RB, Fernández, B, Asch, FM, Barker, AJ, Sierra-Galan, LM, De Kerchove, L, Fernandes, SM, Fedak, PWM, Girdauskas, E, Delgado, V, Abbara, S, Lansac, E, Prakash, SK, Bissell, MM, Popescu, BA, Hope, MD, Sitges, M, Thourani, VH, Pibarot, P, Chandrasekaran, K, Lancellotti, P, Borger, MA, Forrest, JK, Webb, J, Milewicz, DM, Makkar, R, Leon, MB, Sanders, SP, Markl, M, Ferrari, VA, Roberts, WC, Song, JK, Blanke, P, White, CS, Siu, S, Svensson, LG, Braverman, AC, Bavaria, J, Sundt, TM, El Khoury, G, De Paulis, R, Enriquez-Sarano, M, Bax, JJ, Otto, CM & Schäfers, HJ 2021, 'International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes', European Journal of Cardio-thoracic Surgery, vol. 60, no. 3, pp. 448-476. https://doi.org/10.1093/ejcts/ezab038

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes. / Michelena, Hector I.; Della Corte, Alessandro; Evangelista, Arturo et al.
In: European Journal of Cardio-thoracic Surgery, Vol. 60, No. 3, 01.09.2021, p. 448-476.

Research output: Contribution to journal › Article › peer-review

TY - JOUR

T1 - International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes

AU - Michelena, Hector I.

AU - Della Corte, Alessandro

AU - Evangelista, Arturo

AU - Maleszewski, Joseph J.

AU - Edwards, William D.

AU - Roman, Mary J.

AU - Devereux, Richard B.

AU - Fernández, Borja

AU - Asch, Federico M.

AU - Barker, Alex J.

AU - Sierra-Galan, Lilia M.

AU - De Kerchove, Laurent

AU - Fernandes, Susan M.

AU - Fedak, Paul W.M.

AU - Girdauskas, Evaldas

AU - Delgado, Victoria

AU - Abbara, Suhny

AU - Lansac, Emmanuel

AU - Prakash, Siddharth K.

AU - Bissell, Malenka M.

AU - Popescu, Bogdan A.

AU - Hope, Michael D.

AU - Sitges, Marta

AU - Thourani, Vinod H.

AU - Pibarot, Phillippe

AU - Chandrasekaran, Krishnaswamy

AU - Lancellotti, Patrizio

AU - Borger, Michael A.

AU - Forrest, John K.

AU - Webb, John

AU - Milewicz, Dianna M.

AU - Makkar, Raj

AU - Leon, Martin B.

AU - Sanders, Stephen P.

AU - Markl, Michael

AU - Ferrari, Victor A.

AU - Roberts, William C.

AU - Song, Jae Kwan

AU - Blanke, Philipp

AU - White, Charles S.

AU - Siu, Samuel

AU - Svensson, Lars G.

AU - Braverman, Alan C.

AU - Bavaria, Joseph

AU - Sundt, Thoralf M.

AU - El Khoury, Gebrine

AU - De Paulis, Ruggero

AU - Enriquez-Sarano, Maurice

AU - Bax, Jeroen J.

AU - Otto, Catherine M.

AU - Schäfers, Hans Joachim

N1 - Publisher Copyright: © 2021 Jointly between the European Association for Cardio-Thoracic Surgery, The Society of Thoracic Surgeons, the American Association for Thoracic Surgery, and the Radiological Society of North America.

PY - 2021/9/1

Y1 - 2021/9/1

N2 - This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.

AB - This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.

KW - Aortopathy

KW - Bicuspid aortic valve

KW - Classification

KW - Nomenclature

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U2 - 10.1093/ejcts/ezab038

DO - 10.1093/ejcts/ezab038

M3 - Article

C2 - 34293102

AN - SCOPUS:85116542040

SN - 1010-7940

VL - 60

SP - 448

EP - 476

JO - European Journal of Cardio-thoracic Surgery

JF - European Journal of Cardio-thoracic Surgery

IS - 3

ER -

Michelena HI, Della Corte A, Evangelista A, Maleszewski JJ, Edwards WD, Roman MJ et al. International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes. European Journal of Cardio-thoracic Surgery. 2021 Sep 1;60(3):448-476. doi: 10.1093/ejcts/ezab038

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes

Abstract

Keywords

ASJC Scopus subject areas

UN SDGs

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