International Pediatric Otolaryngology Group (IPOG) Consensus Recommendations: Congenital Cholesteatoma

Françoise Denoyelle*, François Simon, Kay W. Chang, Kenny H. Chan, Alan G. Cheng, Alan T. Cheng, Daniel I. Choo, Sam J. Daniel, Anne Farinetti, Erea Noël Garabedian, John H. Greinwald, Stephen R. Hoff, Stephen Hone, Greg R. Licameli, Blake C. Papsin, Dennis S. Poe, Seth Pransky, Richard J.H. Smith, Jean Michel Triglia, Joanna WaltonGeorge Zalzal, Nicolas Leboulanger

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

5 Scopus citations


Objective:To provide recommendations to otolaryngologists and allied physicians for the comprehensive management of children who present with signs and symptoms of congenital cholesteatoma.Methods:A two-iterative Delphi method questionnaire was used to establish expert recommendations by the members of the International Pediatric Otolaryngology Group, on the preoperative work-up, the perioperative considerations, and follow-up.Results:Twenty-two members completed the survey, in 14 tertiary-care center departments representing 5 countries. The main consensual recommendations were: a precise otoscopic description of the quadrants involved, extensive audiological workup (bilateral tonal, vocal audiometry, and BERA), and a CT scan are required. Facial nerve monitoring and a combination of microscope and telescope are recommended for surgical removal. Clinical and audiological follow-up should be pursued yearly for at least 5 years. First MRI follow-up should be done at 18 months postoperatively if the removal violated the matrix. MRI follow-up duration depends on the initial extent of the cholesteatoma.Conclusion:The goal of preoperative and follow-up consensus from International Pediatric Otolaryngology Group participants is to help manage infants and children with congenital cholesteatoma. The operative techniques may vary, and experienced surgeons must perform these procedures.

Original languageEnglish (US)
Pages (from-to)345-351
Number of pages7
JournalOtology and Neurotology
Issue number3
StatePublished - Mar 1 2020


  • Children
  • Congenital cholesteatoma
  • Delphi method
  • IPOG
  • Surgery

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Sensory Systems
  • Clinical Neurology


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