Juvenile xanthogranuloma masquerading as melanoma

Fernandino A. Fontanilla; Deepak P. Edward; Margaret Wong; Howard H. Tessler; Ralph C. Eagle; Debra A. Goldstein

doi:10.1016/j.jaapos.2009.06.010

Juvenile xanthogranuloma masquerading as melanoma

Fernandino A. Fontanilla, Deepak P. Edward, Margaret Wong, Howard H. Tessler, Ralph C. Eagle, Debra A. Goldstein^*

^*Corresponding author for this work

Ophthalmology

Research output: Contribution to journal › Article › peer-review

4 Scopus citations

Abstract

Juvenile xanthogranuloma (JXG) of the uvea is a rare disease that usually responds to systemic steroids or low-dose radiotherapy. We present an atypical case of bilateral JXG involving the entire uveal tract that presented with an aggressive phenotype. The patient was unresponsive to topical and systemic corticosteroids, cyclosporine, and maximal doses of radiation therapy. The disease was ultimately controlled with the alkylating agent chlorambucil.

Original language	English (US)
Pages (from-to)	515-518
Number of pages	4
Journal	Journal of AAPOS
Volume	13
Issue number	5
DOIs	https://doi.org/10.1016/j.jaapos.2009.06.010
State	Published - Oct 2009

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Ophthalmology

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10.1016/j.jaapos.2009.06.010

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title = "Juvenile xanthogranuloma masquerading as melanoma",

abstract = "Juvenile xanthogranuloma (JXG) of the uvea is a rare disease that usually responds to systemic steroids or low-dose radiotherapy. We present an atypical case of bilateral JXG involving the entire uveal tract that presented with an aggressive phenotype. The patient was unresponsive to topical and systemic corticosteroids, cyclosporine, and maximal doses of radiation therapy. The disease was ultimately controlled with the alkylating agent chlorambucil.",

author = "Fontanilla, {Fernandino A.} and Edward, {Deepak P.} and Margaret Wong and Tessler, {Howard H.} and Eagle, {Ralph C.} and Goldstein, {Debra A.}",

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T1 - Juvenile xanthogranuloma masquerading as melanoma

AU - Fontanilla, Fernandino A.

AU - Edward, Deepak P.

AU - Wong, Margaret

AU - Tessler, Howard H.

AU - Eagle, Ralph C.

AU - Goldstein, Debra A.

PY - 2009/10

Y1 - 2009/10

N2 - Juvenile xanthogranuloma (JXG) of the uvea is a rare disease that usually responds to systemic steroids or low-dose radiotherapy. We present an atypical case of bilateral JXG involving the entire uveal tract that presented with an aggressive phenotype. The patient was unresponsive to topical and systemic corticosteroids, cyclosporine, and maximal doses of radiation therapy. The disease was ultimately controlled with the alkylating agent chlorambucil.

AB - Juvenile xanthogranuloma (JXG) of the uvea is a rare disease that usually responds to systemic steroids or low-dose radiotherapy. We present an atypical case of bilateral JXG involving the entire uveal tract that presented with an aggressive phenotype. The patient was unresponsive to topical and systemic corticosteroids, cyclosporine, and maximal doses of radiation therapy. The disease was ultimately controlled with the alkylating agent chlorambucil.

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JO - Journal of AAPOS

JF - Journal of AAPOS

IS - 5

ER -

Juvenile xanthogranuloma masquerading as melanoma

Abstract

ASJC Scopus subject areas

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