Malignant atrophie papulosis (Kohlmeier-Degos disease) is reported for the first time with pathologic verification of central nervous system involvement in a child. The disease began in infancy with rare recurring skin lesions; the child died at the age of 7, after progressive neurologic deterioration. Diagnosis was suspected clinically and confirmed by biopsy of a typical skin lesion. Recognition of this disorder by its dermatologie manifestations may obviate invasive diagnostic procedures.
|Original language||English (US)|
|Number of pages||5|
|State||Published - Apr 1976|
ASJC Scopus subject areas
- Clinical Neurology