Abstract
Malignant atrophie papulosis (Kohlmeier-Degos disease) is reported for the first time with pathologic verification of central nervous system involvement in a child. The disease began in infancy with rare recurring skin lesions; the child died at the age of 7, after progressive neurologic deterioration. Diagnosis was suspected clinically and confirmed by biopsy of a typical skin lesion. Recognition of this disorder by its dermatologie manifestations may obviate invasive diagnostic procedures.
Original language | English (US) |
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Pages (from-to) | 317-321 |
Number of pages | 5 |
Journal | Neurology |
Volume | 26 |
Issue number | 4 |
DOIs | |
State | Published - Apr 1976 |
ASJC Scopus subject areas
- Clinical Neurology