Malignant atrophic papulosis (Kohlmeier-Degos disease) in childhood

Frederick A. Horner*, Gary J. Myers, David A. Stumpf, Bernard J. Oseroff, Byung H. Choi

*Corresponding author for this work

Research output: Contribution to journalArticle

18 Scopus citations

Abstract

Malignant atrophie papulosis (Kohlmeier-Degos disease) is reported for the first time with pathologic verification of central nervous system involvement in a child. The disease began in infancy with rare recurring skin lesions; the child died at the age of 7, after progressive neurologic deterioration. Diagnosis was suspected clinically and confirmed by biopsy of a typical skin lesion. Recognition of this disorder by its dermatologie manifestations may obviate invasive diagnostic procedures.

Original languageEnglish (US)
Pages (from-to)317-321
Number of pages5
JournalNeurology
Volume26
Issue number4
DOIs
StatePublished - Apr 1976

ASJC Scopus subject areas

  • Clinical Neurology

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    Horner, F. A., Myers, G. J., Stumpf, D. A., Oseroff, B. J., & Choi, B. H. (1976). Malignant atrophic papulosis (Kohlmeier-Degos disease) in childhood. Neurology, 26(4), 317-321. https://doi.org/10.1212/wnl.26.4.317