Nutrition management in adults with cystic fibrosis

Jessica M. Shape, Marc A. Sala*

*Corresponding author for this work

Research output: Contribution to journalReview articlepeer-review


Cystic fibrosis (CF) is a lethal, monogenic, autosomal recessive disease with manifestations in multiple organ systems, including the lungs and gastrointestinal tract, that impact adequate nutrition. This review discusses important aspects of nutrition in adults with CF with a focus on exocrine pancreatic insufficiency, CF-related diabetes, and gastrointestinal motility, as well as how advanced lung disease, CF transmembrane conductance regulator modulators, and aging impact nutrition in CF.

Original languageEnglish (US)
Pages (from-to)256-264
Number of pages9
JournalNutrition in Clinical Practice
Issue number2
StatePublished - Apr 2022


  • CFTR modulator
  • cystic fibrosis
  • diabetes mellitus
  • exocrine pancreatic insufficiency
  • gastrointestinal motility
  • lung diseases
  • nutrition status
  • nutrition therapy

ASJC Scopus subject areas

  • Medicine (miscellaneous)
  • Nutrition and Dietetics


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