TY - JOUR
T1 - Oculocutaneous Albinism, Platelet Storage Pool Disease, and Progressive Lupus Nephritis
AU - Bomalaski, John S.
AU - Green, David
AU - Carone, Frank
PY - 1983/4
Y1 - 1983/4
N2 - Systemic lupus erythematosus (SLE) was seen in a patient with oculocutaneous albinism and platelet storage pool disease (Hermansky Pudlak syndrome). Although the patient had severely compromised platelet function, lupus nephritis developed nonetheless, which progressed to end-stage renal disease. The role of platelets in the pathogenesis of the nephritic process is discussed, and it is concluded that release of platelet granular constituents, particularly serotonin, is not required for the microvascular damage of SLE.
AB - Systemic lupus erythematosus (SLE) was seen in a patient with oculocutaneous albinism and platelet storage pool disease (Hermansky Pudlak syndrome). Although the patient had severely compromised platelet function, lupus nephritis developed nonetheless, which progressed to end-stage renal disease. The role of platelets in the pathogenesis of the nephritic process is discussed, and it is concluded that release of platelet granular constituents, particularly serotonin, is not required for the microvascular damage of SLE.
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U2 - 10.1001/archinte.1983.00350040199030
DO - 10.1001/archinte.1983.00350040199030
M3 - Article
C2 - 6340629
AN - SCOPUS:0020741867
VL - 143
SP - 809
EP - 811
JO - Archives of internal medicine (Chicago, Ill. : 1908)
JF - Archives of internal medicine (Chicago, Ill. : 1908)
SN - 2168-6106
IS - 4
ER -