Papular mucinosis (scleromyxoedema) complicating diffuse systemic sclerosis: Clinical features and electron microscope observations

J. Varga*, L. Y. Matsuoka, K. Hashimoto, M. Di Leonardo, S. A. Jimenez

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

9 Scopus citations

Abstract

Papular mucinosis (scleromyxoedema) is an uncommon disorder characterized by generalized papular eruption and cuta neous induration, which may be associated with a variety of extracutaneous manifestations. Although scleroderma and papular mucinosis share many features, they are clinically and histologically distinct entities. We report here a patient with diffuse scleroderma who developed superimposed papular mucinosis. Degranulating mast cells were a prominent ultra- structural finding in the involved skin. The occurrence of scleroderma and papular mucinosis, two uncommon cutaneous indurative diseases, in the same patient has not been described previously.

Original languageEnglish (US)
Pages (from-to)779-782
Number of pages4
JournalRheumatology
Volume31
Issue number11
DOIs
StatePublished - Nov 1992

Funding

ACKNOWLEDGEMENTS This work was supported in part by grant AR 01817 from the National Institutes of Health.

Keywords

  • Cutaneous mucinosis
  • Papular mucinosis
  • Scleromyxoedema
  • Systemic sclerosis

ASJC Scopus subject areas

  • Rheumatology
  • Pharmacology (medical)

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