Progressive maculopathy in a child resulting from vitreopapillary traction on a congenitally anomalous nerve

Ross M. Kennamer-Chapman, Lee M. Jampol, Rithwick Rajagopal*

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

Abstract

To present a case of worsening maculopathy and vision loss due to vitreopapillary traction associated with an anomalous optic nerve head in a pediatric patient successfully managed with pars plana vitrectomy. Methods: Retrospective case report Results: A 13-year-old boy presented with unilateral maculopathy that slowly progressed over a four-year period. As his visual acuity declined, he became increasingly symptomatic. The macular pathology occurred in the setting of vitreopapillary traction overlying multiple congenital optic nerve abnormalities, including a myelinated nerve fiber layer and a Bergmeister papilla. Following pars plana vitrectomy to alleviate the traction, the patient's macular appearance improved, and his vision slowly recovered to baseline. Conclusion: There are limited reports of congenital optic nerve anomalies associated with vitreopapillary traction and maculopathy among any age group. This report illustrates a pediatric case in which removal of traction on the nerve head by pars plana vitrectomy was the key therapeutic intervention to alleviate the maculopathy.

Original languageEnglish (US)
Article number10.1097/ICB.0000000000001666
JournalRetinal Cases and Brief Reports
DOIs
StateAccepted/In press - 2024

Keywords

  • Bergmeister papilla
  • maculopathy
  • myelinated nerve fiber layer
  • vitrectomy

ASJC Scopus subject areas

  • Ophthalmology

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