Abstract
Two patients with severe intrauterine growth retardation and bird-headed appearance are described. These two children had most of the clinical features of the so-called Seckel dwarfism. The radiological findings included: (1) ivory epiphyses affecting all phalanges in one patient and many phalanges in another; (2) cone-shaped epiphyses in the proximal phalanges; (3) marked disharmonic bone maturation between carplas and phalanges, between individual carpals, and from side to side; (4) alteration in the length of the hand bones, with considerable similarity of the metacarpophalangeal pattern between the two children; (5) relatively small carpals, which have an angular configuration; and (6) relatively normal or increased cortical thickness of the metacarpals.
Original language | English (US) |
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Pages (from-to) | 19-24 |
Number of pages | 6 |
Journal | Pediatric radiology |
Volume | 13 |
Issue number | 1 |
DOIs | |
State | Published - Jan 1983 |
Keywords
- Bird-headed dwarfism
- Disharmonic skeletal maturation
- Intrauterine growth retardation
- Ivory epiphyses
- Metacarpophalangeal pattern profile
- Seckel syndrome
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health
- Radiology Nuclear Medicine and imaging