Respiratory improvement by muscle training in adult‐onset acid maltase deficiency

Richard J. Martin*, Robert L. Sufit, Steven P. Ringel, David W. Hudgel, Patricia L. Hill

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

41 Scopus citations

Abstract

A patient with progressive involvement of respiratory function from adult‐onset acid maltase deficiency is reported. The decrement in objective and subjective waking and sleeping respiratory variables was significantly reversed by inspiratory muscle training. This training was accomplished simply by breathing against inspiratory resistors for 15 minutes twice a day. Inspiratory muscle training may prove valuable in other patients with progressive neuromuscular disorders that involve respiratory muscle function.

Original languageEnglish (US)
Pages (from-to)201-203
Number of pages3
JournalMuscle & Nerve
Volume6
Issue number3
DOIs
StatePublished - 1983

ASJC Scopus subject areas

  • Clinical Neurology
  • Physiology (medical)
  • Cellular and Molecular Neuroscience
  • Physiology

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