Association of unilateral severe pulmonary atresia or agenesis and esophageal atresia (EA) with or without tracheoesophageal fistula (TEF) and dextrocardia is a rare and highly lethal combination. We report a case of a full-term female infant who had EA with TEF, right lung agenesis, and dextrocardia. Repair of the fistula took place on day of life 3. We describe anesthetic and surgical concerns of this patient’s case which are keys to a good operative outcome as well as follow-up for the patient.
- Esophageal atresia (EA)
- Lung agenesis
- Tracheoesophageal fistula (TEF)
- Unilateral pulmonary agenesis
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health