Successful hepatic transplantation in congenital absence of recipient portal vein

E. Steve Woodle*, J. R. Thistlethwaite, Jean C. Emond, Peter F. Whitington, Peter Vogelbach, David K. Yousefzadeh, Christoph E. Broelsch

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

82 Scopus citations

Abstract

The first case of hepatic transplantation in a patient with congenital absence of the portal vein (CAPV) is reported. A 10-year-old girl with biliary atresia and CAPV underwent successful hepatic transplantation and has normal liver function 9 months after transplantation. This case is only the seventh reported case of CAPV. Patients with CAPV commonly have additional liver anomalies, cardiac and inferior vena cava anomalies, and polysplenia. Surprisingly, hepatic encephalopathy is not a prominent feature in patients with CAPV despite systemic drainage of mesenteric venous blood. CAPV should not be considered a contraindication to hepatic transplantation.

Original languageEnglish (US)
Pages (from-to)475-479
Number of pages5
JournalSurgery
Volume107
Issue number4
StatePublished - Apr 1990

ASJC Scopus subject areas

  • Surgery

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