TY - JOUR
T1 - Successful hepatic transplantation in congenital absence of recipient portal vein
AU - Woodle, E. Steve
AU - Thistlethwaite, J. R.
AU - Emond, Jean C.
AU - Whitington, Peter F.
AU - Vogelbach, Peter
AU - Yousefzadeh, David K.
AU - Broelsch, Christoph E.
PY - 1990/4
Y1 - 1990/4
N2 - The first case of hepatic transplantation in a patient with congenital absence of the portal vein (CAPV) is reported. A 10-year-old girl with biliary atresia and CAPV underwent successful hepatic transplantation and has normal liver function 9 months after transplantation. This case is only the seventh reported case of CAPV. Patients with CAPV commonly have additional liver anomalies, cardiac and inferior vena cava anomalies, and polysplenia. Surprisingly, hepatic encephalopathy is not a prominent feature in patients with CAPV despite systemic drainage of mesenteric venous blood. CAPV should not be considered a contraindication to hepatic transplantation.
AB - The first case of hepatic transplantation in a patient with congenital absence of the portal vein (CAPV) is reported. A 10-year-old girl with biliary atresia and CAPV underwent successful hepatic transplantation and has normal liver function 9 months after transplantation. This case is only the seventh reported case of CAPV. Patients with CAPV commonly have additional liver anomalies, cardiac and inferior vena cava anomalies, and polysplenia. Surprisingly, hepatic encephalopathy is not a prominent feature in patients with CAPV despite systemic drainage of mesenteric venous blood. CAPV should not be considered a contraindication to hepatic transplantation.
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M3 - Article
C2 - 2321142
AN - SCOPUS:0025264786
SN - 0039-6060
VL - 107
SP - 475
EP - 479
JO - Surgery
JF - Surgery
IS - 4
ER -