Surgery of metabolic liver disease and disorders of biliary transport

Lee M Bass; Riccardo A Superina

doi:10.1201/9781315113791

Surgery of metabolic liver disease and disorders of biliary transport

Research output: Chapter in Book/Report/Conference proceeding › Chapter

Abstract

Byler disease (a form of progressive familial intrahepatic cholestasis [PFIC]) is viewed by many as the prototype for genetic forms of biliary transport disorder. It was first described in the 1960s [3,4] as a cholestatic disease which affected members of the Amish community who were direct descendants of Jacob Byler and Nancy Kaufmann. This couple emigrated to Pennsylvania in the late eighteenth century and were originally from Switzerland.

Original language	English (US)
Title of host publication	Surgery of the Liver, Bile Ducts and Pancreas in Children, Third Edition
Publisher	CRC Press
Pages	151-163
Number of pages	13
ISBN (Electronic)	9781444181210
ISBN (Print)	9781444181203
DOIs	https://doi.org/10.1201/9781315113791
State	Published - Jan 1 2017

Fingerprint

ASJC Scopus subject areas

Medicine(all)

Cite this

Bass, L. M., & Superina, R. A. (2017). Surgery of metabolic liver disease and disorders of biliary transport. In Surgery of the Liver, Bile Ducts and Pancreas in Children, Third Edition (pp. 151-163). CRC Press. https://doi.org/10.1201/9781315113791

@inbook{d2014119fc6c4a90acda3f0bcc4b7dee,

title = "Surgery of metabolic liver disease and disorders of biliary transport",

abstract = "Byler disease (a form of progressive familial intrahepatic cholestasis [PFIC]) is viewed by many as the prototype for genetic forms of biliary transport disorder. It was first described in the 1960s [3,4] as a cholestatic disease which affected members of the Amish community who were direct descendants of Jacob Byler and Nancy Kaufmann. This couple emigrated to Pennsylvania in the late eighteenth century and were originally from Switzerland.",

author = "Bass, {Lee M} and Superina, {Riccardo A}",

year = "2017",

month = jan

day = "1",

doi = "10.1201/9781315113791",

language = "English (US)",

isbn = "9781444181203",

pages = "151--163",

booktitle = "Surgery of the Liver, Bile Ducts and Pancreas in Children, Third Edition",

publisher = "CRC Press",

}

TY - CHAP

T1 - Surgery of metabolic liver disease and disorders of biliary transport

AU - Bass, Lee M

AU - Superina, Riccardo A

PY - 2017/1/1

Y1 - 2017/1/1

N2 - Byler disease (a form of progressive familial intrahepatic cholestasis [PFIC]) is viewed by many as the prototype for genetic forms of biliary transport disorder. It was first described in the 1960s [3,4] as a cholestatic disease which affected members of the Amish community who were direct descendants of Jacob Byler and Nancy Kaufmann. This couple emigrated to Pennsylvania in the late eighteenth century and were originally from Switzerland.

AB - Byler disease (a form of progressive familial intrahepatic cholestasis [PFIC]) is viewed by many as the prototype for genetic forms of biliary transport disorder. It was first described in the 1960s [3,4] as a cholestatic disease which affected members of the Amish community who were direct descendants of Jacob Byler and Nancy Kaufmann. This couple emigrated to Pennsylvania in the late eighteenth century and were originally from Switzerland.

UR - http://www.scopus.com/inward/record.url?scp=85053357850&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=85053357850&partnerID=8YFLogxK

U2 - 10.1201/9781315113791

DO - 10.1201/9781315113791

M3 - Chapter

AN - SCOPUS:85053357850

SN - 9781444181203

SP - 151

EP - 163

BT - Surgery of the Liver, Bile Ducts and Pancreas in Children, Third Edition

PB - CRC Press

ER -

Access to Document

10.1201/9781315113791