The recurrence of the melanotic neuroectodermal tumour of infancy: an unusual presentation of a rare tumour

Antonio Augusto Claudio Pereira*, Mayara Maria de Jesus Rozante, Rafael Bauer Doveinis, Carmine Porcelli Salvarani, Tania Hissa Anegawa, Paola da Costa Souza, Daniel J. Brat, Alessandra Cristina de Oliveira Borges

*Corresponding author for this work

Research output: Contribution to journalArticle

Abstract

The melanotic neuroectodermal tumour of infancy (MNTI), also known as melanotic progonoma, is a rare neoplasm derived from neural crest cells. Although it is fundamentally benign, the tumour may present a locally aggressive behaviour, characterised by a rapid progression and a destructive invasion of adjacent structures, hence causing deformities. Unfortunately, perhaps due to the low incidence of this type of tumour, the published cases in the literature do not characterise the factors that imply the malignant or recurrent behaviour of the disease, nor the therapy to conduct these cases. Here, we report a rare case of a recurrent benign MNTI, approached unusually with a favourable outcome.

Original languageEnglish (US)
Article number1049
Journalecancermedicalscience
Volume14
DOIs
StatePublished - May 26 2020

Keywords

  • Case report
  • Melanotic neuroectodermal tumour of infancy
  • Melanotic progonoma
  • Skull

ASJC Scopus subject areas

  • Oncology
  • Cancer Research

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