TY - JOUR
T1 - The recurrence of the melanotic neuroectodermal tumour of infancy
T2 - an unusual presentation of a rare tumour
AU - Claudio Pereira, Antonio Augusto
AU - de Jesus Rozante, Mayara Maria
AU - Doveinis, Rafael Bauer
AU - Salvarani, Carmine Porcelli
AU - Anegawa, Tania Hissa
AU - da Costa Souza, Paola
AU - Brat, Daniel J.
AU - de Oliveira Borges, Alessandra Cristina
N1 - Publisher Copyright:
© the authors; licensee ecancermedicalscience. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http:// creativecommons.org/licenses/by/3.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
PY - 2020/5/26
Y1 - 2020/5/26
N2 - The melanotic neuroectodermal tumour of infancy (MNTI), also known as melanotic progonoma, is a rare neoplasm derived from neural crest cells. Although it is fundamentally benign, the tumour may present a locally aggressive behaviour, characterised by a rapid progression and a destructive invasion of adjacent structures, hence causing deformities. Unfortunately, perhaps due to the low incidence of this type of tumour, the published cases in the literature do not characterise the factors that imply the malignant or recurrent behaviour of the disease, nor the therapy to conduct these cases. Here, we report a rare case of a recurrent benign MNTI, approached unusually with a favourable outcome.
AB - The melanotic neuroectodermal tumour of infancy (MNTI), also known as melanotic progonoma, is a rare neoplasm derived from neural crest cells. Although it is fundamentally benign, the tumour may present a locally aggressive behaviour, characterised by a rapid progression and a destructive invasion of adjacent structures, hence causing deformities. Unfortunately, perhaps due to the low incidence of this type of tumour, the published cases in the literature do not characterise the factors that imply the malignant or recurrent behaviour of the disease, nor the therapy to conduct these cases. Here, we report a rare case of a recurrent benign MNTI, approached unusually with a favourable outcome.
KW - Case report
KW - Melanotic neuroectodermal tumour of infancy
KW - Melanotic progonoma
KW - Skull
UR - http://www.scopus.com/inward/record.url?scp=85087772924&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=85087772924&partnerID=8YFLogxK
U2 - 10.3332/ECANCER.2020.1049
DO - 10.3332/ECANCER.2020.1049
M3 - Article
AN - SCOPUS:85087772924
SN - 1754-6605
VL - 14
JO - ecancermedicalscience
JF - ecancermedicalscience
M1 - 1049
ER -
