Tricuspid Atresia with Absent Pulmonary Valve with Nearly Discontinuous Branch Pulmonary Arteries

Justin B. Jin; Joshua D. Robinson; Joseph A. Camarda; Michael B. Satzer; Michael R. Carr; Michael Monge; Angira Patel

doi:10.1007/s00246-023-03331-6

Tricuspid Atresia with Absent Pulmonary Valve with Nearly Discontinuous Branch Pulmonary Arteries

Justin B. Jin^*, Joshua D. Robinson, Joseph A. Camarda, Michael B. Satzer, Michael R. Carr, Michael Monge, Angira Patel

^*Corresponding author for this work

Research output: Contribution to journal › Article › peer-review

1 Scopus citations

Abstract

Absent pulmonary valve with tricuspid atresia or tricuspid stenosis (APV-TA/TS) is an extremely rare congenital heart defect associated with significant morbidity and mortality. Compared to Tetralogy of Fallot with Absent Pulmonary Valve Syndrome, branch pulmonary arteries are not typically significantly dilated. We present the case of a newborn male prenatally diagnosed APV-TA with intact ventricular septum (IVS) and nearly discontinuous branch pulmonary arteries, the surgical strategy employed, and the salient hemodynamic factors considered in the medical decision-making.

Original language	English (US)
Pages (from-to)	446-451
Number of pages	6
Journal	Pediatric cardiology
Volume	45
Issue number	2
DOIs	https://doi.org/10.1007/s00246-023-03331-6
State	Published - Feb 2024

Keywords

Absent pulmonary valve
Hypoplastic right ventricle
Interventricular septum
Single ventricle
Tricuspid atresia

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Cardiology and Cardiovascular Medicine

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

Access to Document

10.1007/s00246-023-03331-6

Cite this

@article{fb617e2828bd4abf94d2e1c7536c0a6b,

title = "Tricuspid Atresia with Absent Pulmonary Valve with Nearly Discontinuous Branch Pulmonary Arteries",

abstract = "Absent pulmonary valve with tricuspid atresia or tricuspid stenosis (APV-TA/TS) is an extremely rare congenital heart defect associated with significant morbidity and mortality. Compared to Tetralogy of Fallot with Absent Pulmonary Valve Syndrome, branch pulmonary arteries are not typically significantly dilated. We present the case of a newborn male prenatally diagnosed APV-TA with intact ventricular septum (IVS) and nearly discontinuous branch pulmonary arteries, the surgical strategy employed, and the salient hemodynamic factors considered in the medical decision-making.",

keywords = "Absent pulmonary valve, Hypoplastic right ventricle, Interventricular septum, Single ventricle, Tricuspid atresia",

author = "Jin, \{Justin B.\} and Robinson, \{Joshua D.\} and Camarda, \{Joseph A.\} and Satzer, \{Michael B.\} and Carr, \{Michael R.\} and Michael Monge and Angira Patel",

note = "Publisher Copyright: {\textcopyright} 2023, The Author(s), under exclusive licence to Springer Science+Business Media, LLC, part of Springer Nature.",

year = "2024",

month = feb,

doi = "10.1007/s00246-023-03331-6",

language = "English (US)",

volume = "45",

pages = "446--451",

journal = "Pediatric cardiology",

issn = "0172-0643",

publisher = "Springer",

number = "2",

}

TY - JOUR

T1 - Tricuspid Atresia with Absent Pulmonary Valve with Nearly Discontinuous Branch Pulmonary Arteries

AU - Jin, Justin B.

AU - Robinson, Joshua D.

AU - Camarda, Joseph A.

AU - Satzer, Michael B.

AU - Carr, Michael R.

AU - Monge, Michael

AU - Patel, Angira

PY - 2024/2

Y1 - 2024/2

N2 - Absent pulmonary valve with tricuspid atresia or tricuspid stenosis (APV-TA/TS) is an extremely rare congenital heart defect associated with significant morbidity and mortality. Compared to Tetralogy of Fallot with Absent Pulmonary Valve Syndrome, branch pulmonary arteries are not typically significantly dilated. We present the case of a newborn male prenatally diagnosed APV-TA with intact ventricular septum (IVS) and nearly discontinuous branch pulmonary arteries, the surgical strategy employed, and the salient hemodynamic factors considered in the medical decision-making.

AB - Absent pulmonary valve with tricuspid atresia or tricuspid stenosis (APV-TA/TS) is an extremely rare congenital heart defect associated with significant morbidity and mortality. Compared to Tetralogy of Fallot with Absent Pulmonary Valve Syndrome, branch pulmonary arteries are not typically significantly dilated. We present the case of a newborn male prenatally diagnosed APV-TA with intact ventricular septum (IVS) and nearly discontinuous branch pulmonary arteries, the surgical strategy employed, and the salient hemodynamic factors considered in the medical decision-making.

KW - Absent pulmonary valve

KW - Hypoplastic right ventricle

KW - Interventricular septum

KW - Single ventricle

KW - Tricuspid atresia

UR - http://www.scopus.com/inward/record.url?scp=85176563579&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=85176563579&partnerID=8YFLogxK

U2 - 10.1007/s00246-023-03331-6

DO - 10.1007/s00246-023-03331-6

M3 - Article

C2 - 37955720

AN - SCOPUS:85176563579

SN - 0172-0643

VL - 45

SP - 446

EP - 451

JO - Pediatric cardiology

JF - Pediatric cardiology

IS - 2

ER -

Tricuspid Atresia with Absent Pulmonary Valve with Nearly Discontinuous Branch Pulmonary Arteries

Abstract

Keywords

ASJC Scopus subject areas

UN SDGs

Access to Document

Other files and links

Fingerprint

Cite this