Type 2 Abernethy malformation presenting as a portal vein-coronary sinus fistula

Rohit S. Loomba; Grzegorz W. Telega; Todd M. Gudausky

doi:10.1016/j.jpedsurg.2011.12.031

Type 2 Abernethy malformation presenting as a portal vein-coronary sinus fistula

Rohit S. Loomba^*, Grzegorz W. Telega, Todd M. Gudausky

^*Corresponding author for this work

Pediatrics

Research output: Contribution to journal › Article › peer-review

15 Scopus citations

Abstract

We report the case of a child with Abernethy malformation with an anomalous connection between the portal vein and the coronary sinus. After 30 months of close follow-up, the patient developed hepatoblastoma, a previously documented complication of the Abernethy malformation. This case reports a unique variant of Abernethy malformation and documents the first reported case of hepatoblastoma in a patient with type 2 Abernethy malformation.

Original language	English (US)
Pages (from-to)	E25-E31
Journal	Journal of pediatric surgery
Volume	47
Issue number	5
DOIs	https://doi.org/10.1016/j.jpedsurg.2011.12.031
State	Published - May 2012

Keywords

Congenital absence of the portal vein
Congenital extrahepatic portosystemic shunt
Hepatoblastoma
Portosystemic shunt

ASJC Scopus subject areas

Surgery
Pediatrics, Perinatology, and Child Health

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10.1016/j.jpedsurg.2011.12.031

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title = "Type 2 Abernethy malformation presenting as a portal vein-coronary sinus fistula",

abstract = "We report the case of a child with Abernethy malformation with an anomalous connection between the portal vein and the coronary sinus. After 30 months of close follow-up, the patient developed hepatoblastoma, a previously documented complication of the Abernethy malformation. This case reports a unique variant of Abernethy malformation and documents the first reported case of hepatoblastoma in a patient with type 2 Abernethy malformation.",

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AU - Telega, Grzegorz W.

AU - Gudausky, Todd M.

PY - 2012/5

Y1 - 2012/5

N2 - We report the case of a child with Abernethy malformation with an anomalous connection between the portal vein and the coronary sinus. After 30 months of close follow-up, the patient developed hepatoblastoma, a previously documented complication of the Abernethy malformation. This case reports a unique variant of Abernethy malformation and documents the first reported case of hepatoblastoma in a patient with type 2 Abernethy malformation.

AB - We report the case of a child with Abernethy malformation with an anomalous connection between the portal vein and the coronary sinus. After 30 months of close follow-up, the patient developed hepatoblastoma, a previously documented complication of the Abernethy malformation. This case reports a unique variant of Abernethy malformation and documents the first reported case of hepatoblastoma in a patient with type 2 Abernethy malformation.

KW - Congenital absence of the portal vein

KW - Congenital extrahepatic portosystemic shunt

KW - Hepatoblastoma

KW - Portosystemic shunt

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Type 2 Abernethy malformation presenting as a portal vein-coronary sinus fistula

Abstract

Keywords

ASJC Scopus subject areas

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