XLVIII. The clinical diagnosis of paget's disease of the temporal bone

1. A clinical and historical background of Paget's disease (osteitis deformans) as it relates to the temporal bone has been briefly discussed. 2. The historical and physical data, special audiometric test battery studies, and conventional and tomographic x-ray results in 17 patients with proven Paget's disease and associated hearing loss have been presented. 3. Hearing loss is most frequently of the mixed type. The pure tone configuration is either flat, or has a high frequency drop, the latter being associated with more severe disease. 4. Two patients believed to have otosclerosis of the temporal bone with co-existing Paget's disease elsewhere have been presented with the rationale for differentiation. 5. Paget's disease involving the temporal bone without other skull findings (monostotic) is extremely rare. 6. The facial nerve seems resistant to damage by Paget's disease. 7. In this series vertigo is not too common, is mild and is associated with tomographic findings of demineralization of the semicircular canals.